Acute pancreatitis
Acute pancreatitis a gallstone impacted in the common bile duct beyond the point where the pancreatic duct joins it; 2) heavy alcohol use; 3) systemic disease; 4) trauma; 5) and, in minors, mumps. Acute pancreatitis may be a single event; it may be recurrent; or it may progress to chronic pancreatitis.
Mild cases are usually successfully treated with conservative measures: hospitalization, pain control, nothing by mouth, intravenous nutritional support, and intravenous fluid rehydration. Severe cases often require admission to an intensive care unit to monitor and manage complications of the disease. Complications are associated with a high mortality, even with optimal management.
Signs and symptoms
Common
- severe epigastric pain radiating to the back in 50% of cases
- nausea
- vomiting
- loss of appetite
- fever
- chills
- hemodynamic instability, including shock
- tachycardia
- respiratory distress
- peritonitis
- hiccup
Uncommon
The following are associated with severe disease:- Grey-Turner's sign
- Cullen's sign
- Pleural effusions
- Grünwald sign
- Körte's sign
- Kamenchik's sign
- Mayo-Robson's sign (pain while pressing at the top of the angle lateral to the Erector spinae muscles and below the left 12th rib
- Mayo-Robson's point – a point on border of inner 2/3 with the external 1/3 of the line that represents the bisection of the left upper abdominal quadrant, where tenderness on pressure exists in disease of the pancreas. At this point the tail of pancreas is projected on the abdominal wall.
Complications
Systemic complications include ARDS, multiple organ dysfunction syndrome, DIC, hypocalcemia, hyperglycemia and insulin dependent diabetes mellitus, malabsorption due to exocrine failure
- Metabolic
- Respiratory
- Renal
- * Renal artery or vein thrombosis
- * Kidney failure
- Circulatory
- * Arrhythmias
- * Hypovolemia and shock
- * myocardial infarct
- * Pericardial effusion
- * vascular thrombosis
- Gastrointestinal
- * Gastrointestinal hemorrhage from stress ulceration;
- * gastric varices
- * Gastrointestinal obstruction
- Hepatobiliary
- * Jaundice
- * Portal vein thrombosis
- Neurologic
- * Psychosis or encephalopathy
- * Cerebral Embolism
- * Blindness
- Hematologic
- * Anemia
- * DIC
- * Leucocytosis
- Dermatologic
- * Painful subcutaneous fat necrosis
- Miscellaneous
- * Subcutaneous fat necrosis
- * Arthalgia
Causes
Most common
- Biliary Pancreatitis due to gallstones or constriction of ampulla of Vater in 40% of cases
- Alcohol in 30% of cases
- Idiopathic in 15-25% of cases
- Metabolic disorders: hereditary pancreatitis, hypercalcemia, elevated triglycerides, malnutrition
- Post-ERCP
- Abdominal trauma
- Penetrating ulcers
- Carcinoma of the head of pancreas, and other cancer
- Drugs: diuretics, gliptins, tetracycline, sulfonamides, estrogens, azathioprine and mercaptopurine, pentamidine, salicylates, steroids, Depakote
- Infections: mumps, viral hepatitis, coxsackie B virus, cytomegalovirus, Mycoplasma pneumoniae, Ascaris
- Structural abnormalities: choledochocele, pancreas divisum
- Radiotherapy
- Autoimmune pancreatitis
- Severe Hypertriglyceridemia
Less common
- Scorpion venom
- Chinese liver fluke
- Ischemia from bypass surgery
- Heart valve surgery
- Fat necrosis
- Pregnancy
- Infections other than mumps, including varicella zoster
- Hyperparathyroidism
- Valproic acid
- Cystic fibrosis
- Anorexia or bulimia
- Codeine phosphate reaction
Pathology
Pathogenesis
Acute pancreatitis occurs when there is abnormal activation of digestive enzymes within the pancreas. This occurs through inappropriate activation of inactive enzyme precursors called zymogens inside the pancreas, most notably trypsinogen. Normally, trypsinogen is converted to its active form in the first part of the small intestine, where the enzyme assists in the digestion of proteins. During an episode of acute pancreatitis, trypsinogen comes into contact with lysosomal enzymes, which activate trypsinogen to trypsin. The active form trypsin then leads to further activation of other molecules of trypsinogen. The activation of these digestive enzymes lead to inflammation, edema, vascular injury, and even cellular death. The death of pancreatic cells occurs via two main mechanisms: necrosis, which is less organized and more damaging, or apoptosis, which is more controlled. The balance between these two mechanisms of cellular death is mediated by caspases which regulate apoptosis and have important anti-necrosis functions during pancreatitis: preventing trypsinogen activation, preventing ATP depletion through inhibiting polyADP-ribose polymerase, and by inhibiting the inhibitors of apoptosis. If, however, the caspases are depleted due to either chronic ethanol exposure or through a severe insult then necrosis can predominate.Pathophysiology
The two types of acute pancreatitis are mild and severe, which are defined based on whether the predominant response to cell injury is inflammation or necrosis. In mild pancreatitis, there is inflammation and edema of the pancreas. In severe pancreatitis, there is necrosis of the pancreas, and nearby organs may become injured.As part of the initial injury there is an extensive inflammatory response due to pancreatic cells synthesizing and secreting inflammatory mediators: primarily TNF-alpha and IL-1. A hallmark of acute pancreatitis is a manifestation of the inflammatory response, namely the recruitment of neutrophils to the pancreas. The inflammatory response leads to the secondary manifestations of pancreatitis: hypovolemia from capillary permeability, acute respiratory distress syndrome, disseminated intravascular coagulations, renal failure, cardiovascular failure, and gastrointestinal hemorrhage.
Histopathology
The acute pancreatitis is characterized by acute inflammation and necrosis of pancreas parenchyma, focal enzymic necrosis of pancreatic fat and vessel necrosis. These are produced by intrapancreatic activation of pancreatic enzymes. Lipase activation produces the necrosis of fat tissue in pancreatic interstitium and peripancreatic spaces as well as vessel damage. Necrotic fat cells appear as shadows, contours of cells, lacking the nucleus, pink, finely granular cytoplasm. It is possible to find calcium precipitates. Digestion of vascular walls results in thrombosis and hemorrhage. Inflammatory infiltrate is rich in neutrophils. Due to the pancreas lacking a capsule, the inflammation and necrosis can extend to include fascial layers in the immediate vicinity of the pancreas.Diagnosis
- Acute pancreatitis is diagnosed clinically but requires CT evaluation to differentiate mild acute pancreatitis from severe necrotic pancreatitis. Experienced clinicians were able to detect severe pancreatitis in approximately 34-39% of patients who later had imaging confirmed severe necrotic pancreatitis. Blood studies are used to identify organ failure, offer prognostic information, determine if fluid resuscitation is adequate, and if antibiotics are indicated.
- Blood investigations – Full blood count, renal function tests, liver function, serum calcium, serum amylase and lipase, Arterial blood gas, Trypsin-Selective Test
- Imaging – A triple phase abdominal CT and abdominal ultrasound are together considered the gold standard for the evaluation of acute pancreatitis. Other modalities including the abdominal x-ray lack sensitivity and are not recommended. An important caveat is that imaging during the first 12 hours may be falsely reassuring as the inflammatory and necrotic process usually requires 48 hours to fully manifest.
Differential diagnosis
- Perforated peptic ulcer
- Biliary colic
- Acute cholecystitis
- Pneumonia
- Pleuritic pain
- Myocardial infarction
Biochemical
- Elevated serum amylase and lipase levels, in combination with severe abdominal pain, often trigger the initial diagnosis of acute pancreatitis. However, they have no role in assessing disease severity.
- Serum lipase rises 4 to 8 hours from the onset of symptoms and normalizes within 7 to 14 days after treatment.
- Serum amylase may be normal for cases of acute or chronic pancreatitis and hypertriglyceridemia.
- Reasons for false positive elevated serum amylase include salivary gland disease, bowel obstruction, infarction, cholecystitis, and a perforated ulcer.
- If the lipase level is about 2.5 to 3 times that of amylase, it is an indication of pancreatitis due to alcohol.
- *Decreased serum calcium
- *Glycosuria
Most, but not all individual studies support the superiority of the lipase. In one large study, there were no patients with pancreatitis who had an elevated amylase with a normal lipase. Another study found that the amylase could add diagnostic value to the lipase, but only if the results of the two tests were combined with a discriminant function equation.
While often quoted lipase levels of 3 or more times the upper-limit of normal is diagnostic of pancreatitis, there are also other differential diagnosis to be considered relating to this rise.
Computed tomography
Regarding the need for computed tomography, practice guidelines state:CT is an important common initial assessment tool for acute pancreatitis. Imaging is indicated during the initial presentation if:
- the diagnosis of acute pancreatitis is uncertain
- there is abdominal distension and tenderness, fever >102, or leukocytosis
- there is a Ranson score > 3 or APACHE score > 8
- there is no improvement after 72 hours of conservative medical therapy
- there has been an acute change in status: fever, pain, or shock
- acute change in status
- to determine therapeutic response after surgery or interventional radiologic procedure
- before discharge in patients with severe acute pancreatitis
CT Findings can be classified into the following categories for easy recall:
- Intrapancreatic – diffuse or segmental enlargement, edema, gas bubbles, pancreatic pseudocysts and phlegmons/abscesses
- Peripancreatic / extrapancreatic – irregular pancreatic outline, obliterated peripancreatic fat, retroperitoneal edema, fluid in the lessar sac, fluid in the left anterior pararenal space
- Locoregional – Gerota's fascia sign, pancreatic ascites, pleural effusion, adynamic ileus, etc.
Magnetic resonance imaging
While computed tomography is considered the gold standard in diagnostic imaging for acute pancreatitis, magnetic resonance imaging has become increasingly valuable as a tool for the visualization of the pancreas, particularly of pancreatic fluid collections and necrotized debris. Additional utility of MRI includes its indication for imaging of patients with an allergy to CT's contrast material, and an overall greater sensitivity to hemorrhage, vascular complications, pseudoaneurysms, and venous thrombosis.Another advantage of MRI is its utilization of magnetic resonance cholangiopancreatography sequences. MRCP provides useful information regarding the etiology of acute pancreatitis, i.e., the presence of tiny biliary stones and duct anomalies. Clinical trials indicate that MRCP can be as effective a diagnostic tool for acute pancreatitis with biliary etiology as endoscopic retrograde cholangiopancreatography, but with the benefits of being less invasive and causing fewer complications.
Ultrasound
On abdominal ultrasonography, the finding of a hypoechoic and bulky pancreas is regarded as diagnostic of acute pancreatitis.Treatment
Initial management of a patient with acute pancreatitis consists of supportive care with fluid resuscitation, pain control, nothing by mouth, and nutritional support.Fluid replacement
Aggressive hydration at a rate of 5 to 10 mL/kg per hour of isotonic crystalloid solution to all patients with acute pancreatitis, unless cardiovascular, renal, or other related comorbid factors preclude aggressive fluid replacement. In patients with severe volume depletion that manifests as hypotension and tachycardia, more rapid repletion with 20 mL/kg of intravenous fluid given over 30 minutes followed by 3 mL/kg/hour for 8 to 12 hours.Fluid requirements should be reassessed at frequent intervals in the first six hours of admission and for the next 24 to 48 hours. The rate of fluid resuscitation should be adjusted based on clinical assessment, hematocrit and blood urea nitrogen values.
In the initial stages of acute pancreatitis, fluid replacement has been associated with a reduction in morbidity and mortality.
Pain control
Abdominal pain is often the predominant symptom in patients with acute pancreatitis and should be treated with analgesics.Opioids are safe and effective at providing pain control in patients with acute pancreatitis. Adequate pain control requires the use of intravenous opiates, usually in the form of a patient-controlled analgesia pump. Hydromorphone or fentanyl may be used for pain relief in acute pancreatitis. Fentanyl is being increasingly used due to its better safety profile, especially in renal impairment. As with other opiates, fentanyl can depress respiratory function. It can be given both as a bolus as well as constant infusion.
Meperidine has been historically favored over morphine because of the belief that morphine caused an increase in sphincter of Oddi pressure. However, no clinical studies suggest that morphine can aggravate or cause pancreatitis or cholecystitis. In addition, meperidine has a short half-life and repeated doses can lead to accumulation of the metabolite normeperidine, which causes neuromuscular side effects and, rarely, seizures.
Bowel rest
In the management of acute pancreatitis, the treatment is to stop feeding the patient, giving them nothing by mouth, giving intravenous fluids to prevent dehydration, and sufficient pain control. As the pancreas is stimulated to secrete enzymes by the presence of food in the stomach, having no food pass through the system allows the pancreas to rest. Approximately 20% of patients have a relapse of pain during acute pancreatitis. Approximately 75% of relapses occur within 48 hours of oral refeeding.The incidence of relapse after oral refeeding may be reduced by post-pyloric enteral rather than parenteral feeding prior to oral refeeding. IMRIE scoring is also useful.
Nutritional support
Acute pancreatitis is frequently understood in a catabolic state, characterized by profound metabolic, cardiovascular, pulmonary, hemodynamic, hematological and renal abbretions.Recently, there has been a shift in the management paradigm from TPN to early, post-pyloric enteral feeding. The advantage of enteral feeding is that it is more physiological, prevents gut mucosal atrophy, and is free from the side effects of TPN. The additional advantages of post-pyloric feeding are the inverse relationship of pancreatic exocrine secretions and distance of nutrient delivery from the pylorus, as well as reduced risk of aspiration.
Disadvantages of a naso-enteric feeding tube include increased risk of sinusitis and a still-present risk of accidentally intubating the trachea even in intubated patients.
Oxygen
Oxygen may be provided in some patients if Pao2 levels fall below 70mm of Hg.Antibiotics
Up to 20 percent of people with acute pancreatitis develop an infection outside the pancreas such as bloodstream infections, pneumonia, or urinary tract infections. These infections are associated with an increase in mortality. When an infection is suspected, antibiotics should be started while the source of the infection is being determined. However, if cultures are negative and no source of infection is identified, antibiotics should be discontinued.Preventative antibiotics are not recommended in people with acute pancreatitis, regardless of the type or disease severity
ERCP
If a gallstone is detected, Endoscopic retrograde cholangiopancreatography, performed within 24 to 72 hours of presentation with successful removal of the stone, is known to reduce morbidity and mortality. The indications for early ERCP are:- Clinical deterioration or lack of improvement after 24 hours
- Detection of common bile duct stones or dilated intrahepatic or extrahepatic ducts on abdominal CT
Surgery
Surgery is indicated for infected pancreatic necrosis and diagnostic uncertainty and complications. The most common cause of death in acute pancreatitis is secondary infection. Infection is diagnosed based on 2 criteria- Gas bubbles on CT scan
- Positive bacterial culture on FNA of the pancreas.
- Minimally invasive management – necrosectomy through small incision in skin or abdomen
- Conventional management – necrosectomy with simple drainage
- Closed management – necrosectomy with closed continuous postoperative lavage
- Open management – necrosectomy with planned staged reoperations at definite intervals
Other measures
- Pancreatic enzyme inhibitors are proven not to work.
- The use of octreotide has been shown not to improve outcomes.
Classification by severity: prognostic scoring systems
Some may develop abscess, pseudocyst or duodenal obstruction.
In 5 percent cases, it may result in ARDS, DIC
Acute pancreatitis can be further divided into mild and severe pancreatitis.
Mostly the Ranson Criteria are used to determine severity of acute pancreatitis. In severe pancreatitis serious amounts of necrosis determine the further clinical outcome. About 20% of the acute pancreatitis are severe with a mortality of about 20%. This is an important classification as severe pancreatitis will need intensive care therapy whereas mild pancreatitis can be treated on the common ward.
Necrosis will be followed by a systemic inflammatory response syndrome and will determine the immediate clinical course. The further clinical course is then determined by bacterial infection. SIRS is the cause of bacterial translocation from the patients colon.
There are several ways to help distinguish between these two forms. One is the above-mentioned Ranson Score.
In predicting the prognosis, there are several scoring indices that have been used as predictors of survival. Two such scoring systems are the Ranson criteria and APACHE II indices. Most, but not all studies report that the Apache score may be more accurate. In the negative study of the APACHE-II, the APACHE-II 24-hour score was used rather than the 48-hour score. In addition, all patients in the study received an ultrasound twice which may have influenced allocation of co-interventions. Regardless, only the APACHE-II can be fully calculated upon admission. As the APACHE-II is more cumbersome to calculate, presumably patients whose only laboratory abnormality is an elevated lipase or amylase do not need assessment with the APACHE-II; however, this approach is not studied. The APACHE-II score can be calculated at .
Practice guidelines state:
Ranson score
The Ranson score is used to predict the severity of acute pancreatitis. They were introduced in 1974.At admission
- age in years > 55 years
- white blood cell count > 16000 cells/mm3
- blood glucose > 11.1 mmol/L
- serum AST > 250 IU/L
- serum LDH > 350 IU/L
At 48 hours
- Calcium
- Hematocrit fall >10%
- Oxygen
- BUN increased by 1.8 or more mmol/L after IV fluid hydration
- Base deficit > 4 mEq/L
- Sequestration of fluids > 6 L
Alternatively, pancreatitis can be diagnosed by meeting any of the following:
Alternative Ranson score
of ≥ 8Organ failure
Substantial pancreatic necrosis
Interpretation
If the score ≥ 3, severe pancreatitis likely.
If the score < 3, severe pancreatitis is unlikely
Or
Score 0 to 2 : 2% mortality
Score 3 to 4 : 15% mortality
Score 5 to 6 : 40% mortality
Score 7 to 8 : 100% mortality
APACHE II score
"Acute Physiology And Chronic Health Evaluation" score > 8 points predicts 11% to 18% mortality- Hemorrhagic peritoneal fluid
- Obesity
- Indicators of organ failure
- Hypotension or tachycardia > 130 beat/min
- PO2 <60 mmHg
- Oliguria or increasing BUN and creatinine
- Serum calcium < 1.90 mmol/L or serum albumin <33 g/L >
Balthazar score
Balthazar grade
Balthazar grade | Appearance on CT | CT grade points |
Grade A | Normal CT | 0 points |
Grade B | Focal or diffuse enlargement of the pancreas | 1 point |
Grade C | Pancreatic gland abnormalities and peripancreatic inflammation | 2 points |
Grade D | Fluid collection in a single location | 3 points |
Grade E | Two or more fluid collections and / or gas bubbles in or adjacent to pancreas | 4 points |
Necrosis score
Necrosis percentage | Points |
No necrosis | 0 points |
0 to 30% necrosis | 2 points |
30 to 50% necrosis | 4 points |
Over 50% necrosis | 6 points |
CTSI's staging of acute pancreatitis severity has been shown by a number of studies to provide more accurate assessment than APACHE II, Ranson, and C-reactive protein level. However, a few studies indicate that CTSI is not significantly associated with the prognosis of hospitalization in patients with pancreatic necrosis, nor is it an accurate predictor of AP severity.
Glasgow score
The Glasgow score is valid for both gallstone and alcohol induced pancreatitis, whereas the Ranson score is only for alcohol induced pancreatitis. If a patient scores 3 or more it indicates severe pancreatitis and the patient should be considered for transfer to ITU. It is scored through the mnemonic, PANCREAS:- P - PaO2 <8kPa
- A - Age >55-years-old
- N - Neutrophilia: WCC >15x10/L
- C - Calcium <2 mmol/L
- R - Renal function: Urea >16 mmol/L
- E - Enzymes: LDH >600iu/L; AST >200iu/L
- A - Albumin <32g/L
- S - Sugar: blood glucose >10 mmol/L
BISAP score
- BUN >25 mg/dL
- Abnormal mental status with a Glasgow coma score <15
- Evidence of SIRS
- Patient age >60 years old
- Imaging study reveals pleural effusion
Epidemiology
In the United States, the annual incidence is 18 cases of acute pancreatitis per 100,000 population, and it accounts for 220,000 hospitalizations in the US. In a European cross-sectional study, incidence of acute pancreatitis increased from 12.4 to 15.9 per 100,000 annually from 1985 to 1995; however, mortality remained stable as a result of better outcomes. Another study showed a lower incidence of 9.8 per 100,000 but a similar worsening trend over time.In Western countries, the most common cause is alcohol, accounting for 65 percent of acute pancreatitis cases in the US, 20 percent of cases in Sweden, and 5 percent of those in the United Kingdom. In Eastern countries, gallstones are the most common cause of acute pancreatitis. The causes of acute pancreatitis also varies across age groups, with trauma and systemic disease being more common in children. Mumps is a more common cause in adolescents and young adults than in other age groups.